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Systemic Lupus Erythematosus: Implications for Health Psychology
Dudley Ames
Forest Institute of Professional Psychology
Springfield, MO

Definition of Disease/Condition:
Systemic lupus erythematosus (SLE), a chronic autoimmune disease, can cause various problems such as inflammation, rashes, arthritis, anemia, seizures, and psychiatric illness and often affects the internal organs. The disease mimics so many disorders it has been misdiagnosed as everything from rheumatoid arthritis to schizophrenia (Kotzin, 1993).

With lupus, as well as with other autoimmune disorders, the immune system loses its ability to tell the difference between its own cells and tissues, and foreign substances (antigens). When this happens, autoantibodies are produced which in turn attack the body's own cells and tissues, causing pain and inflammation. In addition, some autoantibodies join with substances from the body's own cells or tissues to form molecules, called immune complexes, which build up in the body and contribute to inflammation and tissue injury.

In 1982, the American College of Rheumatology revised the criteria for the diagnosis of SLE (Tan et al., 1982). If a patient displays four or more of the following symptoms (either serially or simultaneously), the patient may be diagnosed with SLE: (a) a red rash over cheeks and the bridge of the nose (malar rash); (b) a red, scaly rash on the face, scalp, ears, arms, or chest (discoid rash);(c) an unusual reaction to the sun (photosensitivity); (d) small sores (oral ulcers) on the moist lining of the nose or mouth; (e) arthritis characterized by tenderness, swelling or fluid in two or more peripheral joints; (f) documented pleuritis or pericarditis; (g) excessive protein and/or cellular casts in the urine; (h) seizures and/or psychosis (not accounted for by drug reactions or identified metabolic disorders); (I) a decrease in the number of red and white blood cells or platelets; (j) immunologic disorder (blood test indicates positive LE cell preparation, anti-DNA, positive anti-Sm or false positive syphilis test); (k) positive ANA blood test.

The exact cause of lupus is not known, though there is likely an interaction between multiple susceptibility genes and environmental elements. Wallace (1995) believes that of those who carry lupus genes, only 10% will ever develop the disease. SLE is a serious, chronic disease, and the management of the illness is a complex task involving a number of medical decisions.

Incidence/Prevalence:
Wallace (1995) stated that surveys indicate an incidence of between 1.8 and 7.6 per 100,000 population (new cases per year) in the United States, that 80% of those afflicted are diagnosed between the ages of 15 and 45, and close to 90% of those are women. Hochberg (1997) wrote that the overall prevalence of SLE in the U.S. has been reported to range between 14.6 and 50.8 cases per 100,000 persons. Studies vary widely over time, place, population, and method of ascertaining cases. Data suggests that the prevalence of SLE in the U.S. may be greater than has been previously reported.

Estimated dollar cost to public health:
In a major study, Hoffman, Rice, and Sung (1996) determined that as of 1990 there were more than 90 million Americans living with chronic conditions. They found that the annual cost in 1990 amounted to $659 billion. This included $459 billion for direct health care costs and $234 billion in indirect costs to society, including loss of work time and early death. There are 1.5 million lupus patients in the U.S., by conservative estimate. If they incur an equivalent portion of the health care costs, then the total cost of the disease (both direct and indirect) would be approximately $11 billion per year.

Morbidity and mortality:
In their review of the diagnosis and management of SLE, Boumpas et al. (1995) reported 5-year survival rates of 90% or more and 10-year survival rates of more than 80%. More than 90% of patients with SLE die from one of five causes: complication of kidney disease, infections, central nervous system lupus, blood clots, or cardiovascular complications. Deaths from lupus tend to occur either early in the course of the disease, among those who have active aggressive lupus and do not respond well to treatment, or after 15 to 20 years from continuously active inflammation or complications of therapy (Wallace, 1995).

Medical costs which could be offset by psychological interventions:
In recent years, numerous researchers have noted that SLE carries with it major components that are psychological in nature. There is considerable evidence that patients with SLE are likely to experience psychological dysfunction, especially related to depression. This is an area where psychologists can be particularly effective with patient education. Several studies have shown that patient education programs can reduce health care costs from 10% to 20%, saving up to $2.50 in medical costs for every $1.00 spent on education programs.

New treatments and breakthroughs in this disease/condition:
New drugs that hold the promise of greater effectiveness and fewer side effects are being developed and tested. The possibility of reconstructing the immune system by bone marrow transplantation is being explored. And the National Institutes of Health announced that researchers have localized a gene, on the long arm of human chromosome 1, that predisposes people to SLE (Ben-Ari, 1997). Continuing to identify genes for lupus will provide new insights about why people get the disease and should aid the development of new treatments and/or preventive measures.

Marketing plan for psychologists to include this area of expertise in their practice:
The American Psychological Association (1995) notes that 63% of adults say they would prefer to see a physician who works with a psychologist. Many physicians who treat lupus are already seeking a multi-disciplinary treatment team approach. Psychologists who wish to work with SLE patients should be prepared to help them reduce stress, better their sleeping habits, and increase their social support, possibly through the use of group therapy. They should utilize education programs that teach proper diet and exercise, chronic pain management, and effective coping skills. They should approach this field using a targeted, behavioral, health psychology approach rather than with the idea of doing long-term psychotherapy.

Perhaps the single most important thing that psychologists can do to market their skills in this area is to carefully study the literature on SLE. Armed with the information about the disease itself and the areas in which psychologists may be of assistance, they will be better prepared to "sell" the idea of a multi-discipline approach to physicians who treat lupus.


References:
Ben-Ari, A. (1997). Researchers locate lupus gene on chromosome 1 [On-line]. Available:
http://www.nih.gov/news/pr/feb97/niams-19.htm

Boumpas, D. T., Austin, H. A., Fessler, B. J., Balow, J. E., Klippel, J. H., & Lockshin, M. D. (1995). Systemic lupus erythematosus: Emerging concepts. Annals of Internal Medicine,
122, 940-50.

Hochberg, M. C. (1997). The epidemiology of systemic lupus erythematosus. In D. J. Wallace, & B. H. Hahn (Eds.), Dubois' lupus erythematosus (pp. 49-65). Baltimore: Williams & Wilkins.

Hoffman, C., Rice, D., Sung, H. (1996). Persons with chronic conditions: Their prevalence and costs. The Journal of the American Medical Association, 276, 1473-1479.

Kotzin, B. L. (1993). Tracking and treating lupus--the great impostor. Medical/Scientific Update [On-line], 9(4). Available:
http://www.njc.org/MSU/09n4MSU_Lupus.html

Tan, E. M., Cohen, A. S., Fries, J. F., Masi, A. T., McShane, D. J., Rothfield, N. F., Schaller, J. G., Talal, N., & Winchester, R. J. (1982). The 1982 revised criteria for the classification of systemic lupus erythematosus. Arthritis & Rheumatism, 25(11), 1271-1277.

Wallace, D. J. (1995). The lupus book: A guide for patients and their families. New York: Oxford University Press.


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